Thoracic Insufficiency Syndrome: Pulmonary Problems Related to Chest and Spine Deformity in Children

Overview

Chest and spine deformity in the first decade of life can lead to severe restrictive lung disease. Associated etiologies include congenital malformations of the spine and thorax, neuromuscular conditions, and skeletal dysplasias. Care and treatment involve a multidisciplinary approach. CHOP has utilized cutting edge pathways and technologies to assess and manage this diverse group of patients.

Learning objectives

1. Understand the natural history of early-onset scoliosis
2. Understand the impact of spine deformity on pulmonary development and function
3. Understand assessment of pulmonary function in young children with restrictive lung disease

Speakers

Patrick J. Cahill, MD, is an attending physician in the Division of Orthopaedics and the Robert M. Campbell Jr. Endowed Chair in Thoracic Insufficiency Syndrome at Children's Hospital of Philadelphia.

Oscar H. Mayer, MD, is an attending physician in the Division Pulmonary and Sleep Medicine and Director of the Pulmonary Function Laboratory at Children's Hospital of Philadelphia.

Moderator

Jason B. Anari, MD, is an attending physician with the Division of Orthopaedics, specializing in the treatment of spine disorders in children at Children's Hospital of Philadelphia.

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ACCME Accreditation Statement: Children’s Hospital of Philadelphia is accredited by the Accreditation Council for Continuing Medical Education (ACCME) to provide continuing medical education for physicians.

Approval of AMA PRA Category 1 Credit(s) for this lecture is pending. If approved, physicians can claim CME credit commensurate with the extent of their participation in the activity for free.

Related specialties: orthopaedics, general pediatrics